05Enfermedades endocrinas, nutricionales o metabólicas
Trastornos metabólicos
Errores congénitos del metabolismo
5C50Errores congénitos del metabolismo de los aminoácidos u otros ácidos orgánicos
5C50.0Fenilcetonuria
5C50.01
category
Fenilcetonuria atípica
Definition Forma infrecuente de fenilcetonuria (error congénito del metabolismo del aminoácido fenilalanina) caracterizada por síntomas leves o moderados de fenilcetonuria.
Also indexed as
FCU -[fenilcetonuria] atípica Fenilcetonuria atípica Fenilcetonuria no clásica
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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