Extranodal marginal zone B-cell lymphoma, primary site skin

Definition

A low-grade, extranodal marginal zone B-cell lymphoma of the mucosa-associated lymphoid tissue that arises from the skin. It usually presents with multifocal papular or nodular lesions in the arms or trunk. It rarely disseminates to internal organs or progresses to high grade lymphoma.

Also indexed as

Nearby in Other specified mature B-cell neoplasms or lymphoma

• 2A85.0Nodal marginal zone lymphoma
• 2A85.1Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach
• 2A85.3Extranodal marginal zone B-cell lymphoma, primary site excluding stomach or skin
• 2A85.4Lymphoplasmacytic lymphoma
• 2A85.5Mantle cell lymphoma
• 2A85.6Burkitt lymphoma including Burkitt leukaemia
• 4B4YOther specified diseases of the immune system