Nodal marginal zone lymphoma

Definition

A primary nodal B-cell non-Hodgkin lymphoma which morphologically resembles lymph nodes involved by marginal zone lymphomas of extranodal or splenic types, but without evidence of extranodal or splenic disease. This is a rare entity, and most patients present with localised or generalised lymphadenopathy. The clinical course is indolent.

Also indexed as

Nearby in Other specified mature B-cell neoplasms or lymphoma

• 2A85.1Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach
• 2A85.2Extranodal marginal zone B-cell lymphoma, primary site skin
• 2A85.3Extranodal marginal zone B-cell lymphoma, primary site excluding stomach or skin
• 2A85.4Lymphoplasmacytic lymphoma
• 2A85.5Mantle cell lymphoma
• 2A85.6Burkitt lymphoma including Burkitt leukaemia
• 4B4YOther specified diseases of the immune system