Heavy chain diseases or malignant immunoproliferative diseases

Definition

A group of rare disorders of immunoglobulin synthesis associated with B-cell proliferative disorders that produce monoclonal heavy chains and typically no light chains.

5 subordinate codes

• 2A84.0Alpha heavy chain disease
• 2A84.1Gamma heavy chain disease
• 2A84.2Mu heavy chain disease
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Mature B-cell neoplasms

• 2A80Follicular lymphoma
• 2A81Diffuse large B-cell lymphomas
• 2A82Mature B-cell neoplasm with leukaemic behaviour
• 2A83Plasma cell neoplasms
• 2A85Other specified mature B-cell neoplasms or lymphoma
• 2A86B-cell lymphoma, mixed features
• 4B4ZDiseases of the immune system, unspecified