A clonal disorder characterised by the secretion of a truncated gamma chain. In most cases, it is associated with morphologic changes also seen in lymphoplasmacytic lymphomas, but the clinical course is typically more aggressive than in lymphoplasmacytic lymphoma/Waldenstrom's macroglobulinemia.
Inclusions
Franklin disease
Also indexed as
Franklin diseaseGamma heavy chain disease
Nearby in Heavy chain diseases or malignant immunoproliferative diseases