ICD·index Chapters ENESDE
CB04.31 category

Pulmonary alveolar proteinosis

Definition

This is a rare lung disease in which abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily in the settings of malignancy (especially in myeloid leukemia), pulmonary infection, or environmental exposure to dusts or chemicals.

Also indexed as

Autoimmune pulmonary alveolar proteinosisCongenital pulmonary alveolar proteinosisIdiopathic alveolar lipoproteinosisIdiopathic pulmonary alveolar proteinosisPulmonary alveolar proteinosisSecondary pulmonary alveolar proteinosis

Nearby in Alveolar or peri-alveolar conditions