Lymphangioleiomyomatosis

Definition

Lymphangioleiomyomatosis (LAM) is a multiple cystic lung disease characterised by progressive cystic destruction of the lung and lymphatic abnormalities, frequently associated with renal angiomyolipomas (AMLs). LAM occurs either sporadically or as a manifestation of tuberous sclerosis complex (TSC).

4 subordinate codes

• CB07.0Lymphangioleiomyomatosis associated with tuberous sclerosis complex
• CB07.1Sporadic lymphangioleiomyomatosis
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Respiratory diseases principally affecting the lung interstitium

• CB00Acute respiratory distress syndrome
• CB01Pulmonary oedema
• CB02Pulmonary eosinophilia
• CB03Idiopathic interstitial pneumonitis
• CB04Primary interstitial lung diseases specific to infancy or childhood
• CB05Interstitial lung diseases associated with systemic diseases
• CB06Pulmonary alveolar microlithiasis
• 4B4YOther specified diseases of the immune system