Pulmonary capillaritis

Definition

Isolated pauciimmune pulmonary capillaritis is a small vessel vasculitis restricted to the lungs that may induce diffuse alveolar haemorrhage with dyspnoea, anaemia, chest pain, haemoptysis, bilateral and diffuse alveolar infiltrates at chest X-rays, without any underlying systemic disease. ANCA are frequently positive but could be negative.

Also indexed as

Nearby in Primary interstitial lung diseases specific to infancy or childhood

• CB04.0Diffuse pulmonary developmental disorders
• CB04.1Pulmonary lymphatic dysplasia syndromes
• CB04.2Disorders of surfactant metabolism
• CB04.3Alveolar or peri-alveolar conditions
• CB04.5Brain-lung-thyroid syndrome
• CB04.6Chronic pneumonitis of infancy
• CB04.7Neuroendocrine cell hyperplasia of infancy
• 4B4YOther specified diseases of the immune system