Chronic pneumonitis of infancy

Definition

Chronic pneumonitis of infancy is a rare paediatric form of interstitial lung disease (ILD) sharing clinical and radiologic features with other forms of ILD (cough, tachypnoea, and infiltrative opacities on chest imaging) and harbouring specific histological abnormalities including diffuse thickening of alveolar septa, hyperplasia of type 2 alveolar epithelial cells (AEC), and presence of primitive mesenchymal cells within the alveolar septa.

Also indexed as

Nearby in Primary interstitial lung diseases specific to infancy or childhood

• CB04.0Diffuse pulmonary developmental disorders
• CB04.1Pulmonary lymphatic dysplasia syndromes
• CB04.2Disorders of surfactant metabolism
• CB04.3Alveolar or peri-alveolar conditions
• CB04.4Pulmonary capillaritis
• CB04.5Brain-lung-thyroid syndrome
• CB04.7Neuroendocrine cell hyperplasia of infancy
• 4B4YOther specified diseases of the immune system