Systemic Epstein-Barr Virus-positive T-cell lymphoma of childhood

Definition

This neoplasm of childhood is characterised by a clonal proliferation of EBV-infected T-cells with an activated cytotoxic phenotype. It can occur shortly after primary acute EBV infection or in the setting of chronic active EBV infection (CAEBV).

Also indexed as

Nearby in Mature T-cell lymphoma, specified types, nodal or systemic

• 2A90.0T-cell prolymphocytic leukaemia
• 2A90.1T-cell large granular lymphocytic leukaemia
• 2A90.2Chronic lymphoproliferative disorders of NK-cells
• 2A90.3Aggressive NK cell leukaemia
• 2A90.5Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated
• 2A90.6Extranodal NK/T-cell lymphoma, nasal type
• 2A90.7Enteropathy associated T-cell lymphoma
• 2A90.8Hepatosplenic T-cell lymphoma