2A81.9
category
Primary effusion lymphoma
Definition
An aggressive non-Hodgkin B-cell lymphoma composed of large cells, presenting as a serous effusion without detectable tumour masses. It is universally associated with human herpes virus 8 (HHV-8)/Kaposi sarcoma herpes virus (KSHV) [HHV-8/KSHV]. It mostly occurs in the setting of immunodeficiency; most cases have been reported in HIV positive patients. The most common sites of involvement are the pleural, pericardial, and peritoneal cavities. The prognosis is extremely unfavorable.
Also indexed as
Primary effusion lymphomaPrimary effusion lymphoma associated with the human immune deficiency virus infection
Nearby in Diffuse large B-cell lymphomas
2A81.0Primary mediastinal large B-cell lymphoma2A81.1Intravascular large B-cell lymphoma2A81.2Plasmablastic lymphoma2A81.3Lymphomatoid granulomatosis2A81.4T-cell/histiocyte rich large B-cell lymphoma2A81.5Primary diffuse large B-cell lymphoma of central nervous system2A81.6Epstein-Barr Virus-positive diffuse large B-cell lymphoma of the elderly2A81.7Diffuse large B-cell lymphoma associated with chronic inflammation