Juvenile myelomonocytic leukaemia

Definition

A myelodysplastic/myeloproliferative neoplasm of childhood that is characterised by proliferation principally of the granulocytic and monocytic lineages. Myelomonocytic proliferation is seen in the bone marrow and the blood. The leukemic cells may infiltrate any tissue, however liver, spleen, lymph nodes, skin, and respiratory tract are the most common sites of involvement.

3 subordinate codes

• 2A42.0Juvenile myelomonocytic leukaemia in complete remission
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Myelodysplastic and myeloproliferative neoplasms

• 2A40Chronic myelomonocytic leukaemia
• 2A41Atypical chronic myeloid leukaemia, BCR-ABL1-negative
• 2A43Refractory anaemia with ring sideroblasts associated with marked thrombocytosis
• 2A44Myeloproliferative and myelodysplastic disease, unclassifiable
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified