3A20.3
category
Paroxysmal cold haemoglobinuria
Definition
Paroxysmal cold hemoglobinuria is a very rare subtype of autoimmune haemolytic anaemia (AIHA), caused by the presence of cold-reacting autoantibodies in the blood and characterised by the sudden presence of hemoglobinuria, typically after exposure to cold temperatures. PCH is thought to account for at most 2-10% of cases of AIHA.
Also indexed as
Donath-Landsteiner syndromeParoxysmal cold haemoglobinuria
Nearby in Acquired haemolytic anaemia, immune
3A20.0Autoimmune haemolytic anaemia, warm type3A20.1Autoimmune haemolytic anaemia, cold type3A20.2Autoimmune haemolytic anaemia, mixed type, cold and warm3A20.4Alloimmune haemolytic anaemia3A20.5Evans syndrome4B4YOther specified diseases of the immune system4B4ZDiseases of the immune system, unspecified