ICD·index Chapters ENESDE
LD24.C category

Bent bone dysplasias

Definition

Any syndromes are characterised by poor mineralization of the skull, craniosynostosis, hypoplastic pubis and clavicles, osteopenia, bent long bones, low-set ears, hypertelorism, midface hypoplasia, prematurely erupted fetal teeth, and micrognathia. These syndromes may be associated with mutation of the FGFR2 gene.

Also indexed as

Bent bone dysplasiasCampomelia, Cumming typeKyphomelic dysplasiaStüve-Wiedemann syndromeWeismann-Netter syndrome

Nearby in Syndromes with skeletal anomalies as a major feature