Congenital hydrocephalus

Definition

A disease caused by failure of the brain to correctly develop during the antenatal period. This condition is characterised by a rapid increase in head circumference or an unusually large head size due to excessive accumulation of cerebrospinal fluid in the brain. This condition may also present with vomiting, sleepiness, irritability, downward deviation of the eyes, or seizures. Confirmation is through observation of cerebrospinal fluid within cerebral ventricles by imaging.

Inclusions

• Hydrocephalus in newborn

Exclusions

• Arnold-Chiari malformation type I (LA07.4)
• Arnold-Chiari malformation type II (LA03)
• Hydrocephalus due to congenital toxoplasmosis (KA64.0)
• Myelomeningocele with hydrocephalus (LA02.00)

3 subordinate codes

• LA04.0Hydrocephalus with stenosis of the aqueduct of Sylvius
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Structural developmental anomalies of the nervous system

• LA00Anencephaly or similar anomalies
• LA01Cephalocele
• LA02Spina bifida
• LA03Arnold-Chiari malformation type II
• LA05Cerebral structural developmental anomalies
• LA06Cerebellar structural developmental anomalies
• LA07Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
• 4B4YOther specified diseases of the immune system