Anencephaly or similar anomalies

Definition

A malformation of the nervous system caused by the failure of neuropore closure. Infants are born with intact spinal cord, cerebellum, and brainstem, but lack formation of neural structures above this level. The skull is only partially formed but the eyes are usually normal.

6 subordinate codes

• LA00.0Anencephaly
• LA00.1Iniencephaly
• LA00.2Acephaly
• LA00.3Amyelencephaly
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Structural developmental anomalies of the nervous system

• LA01Cephalocele
• LA02Spina bifida
• LA03Arnold-Chiari malformation type II
• LA04Congenital hydrocephalus
• LA05Cerebral structural developmental anomalies
• LA06Cerebellar structural developmental anomalies
• LA07Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
• 4B4YOther specified diseases of the immune system