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Chapters ENES DE

20Developmental anomalies
Structural developmental anomalies primarily affecting one body system
Structural developmental anomalies of the nervous system
LA00Anencephaly or similar anomalies

LA00.2 category

Acephaly

Also indexed as

AcephaliaAcephalismAcephalyCongenital absence of head

Nearby in Anencephaly or similar anomalies

LA00.0Anencephaly
LA00.1Iniencephaly
LA00.3Amyelencephaly
4B4YOther specified diseases of the immune system
4B4ZDiseases of the immune system, unspecified

PreviousLA00.1 — Iniencephaly NextLA00.3 — Amyelencephaly

Browse ICD-11

01Certain infectious or parasitic diseases
02Neoplasms
03Diseases of the blood or blood-forming organs
04Diseases of the immune system
05Endocrine, nutritional or metabolic diseases
06Mental, behavioural or neurodevelopmental disorders
07Sleep-wake disorders
08Diseases of the nervous system
09Diseases of the visual system
10Diseases of the ear or mastoid process
11Diseases of the circulatory system
12Diseases of the respiratory system
13Diseases of the digestive system
14Diseases of the skin
15Diseases of the musculoskeletal system or connective tissue
16Diseases of the genitourinary system
17Conditions related to sexual health
18Pregnancy, childbirth or the puerperium
19Certain conditions originating in the perinatal period
20Developmental anomalies
21Symptoms, signs or clinical findings, not elsewhere classified
22Injury, poisoning or certain other consequences of external causes
23External causes of morbidity or mortality
24Factors influencing health status or contact with health services
25Codes for special purposes
26Supplementary Chapter Traditional Medicine Conditions
VSupplementary section for functioning assessment
XExtension Codes
LA00-LD0ZStructural developmental anomalies primarily affecting one body system
LD20-LD2ZMultiple developmental anomalies or syndromes
LD40-LD7ZChromosomal anomalies, excluding gene mutations
LD90Conditions with disorders of intellectual development as a relevant clinical feature
4B4YOther specified diseases of the immune system
4B4ZDiseases of the immune system, unspecified
LA00-LA0ZStructural developmental anomalies of the nervous system
LA10-LA1ZStructural developmental anomalies of the eye, eyelid or lacrimal apparatus
LA20-LA2ZStructural developmental anomalies of the ear
LA30-LA5ZStructural developmental anomalies of the face, mouth or teeth
LA60-LA6ZStructural developmental anomalies of the neck
LA70-LA7ZStructural developmental anomalies of the respiratory system
LA80-LA9ZStructural developmental anomalies of the circulatory system
LB00-LB0ZStructural developmental anomalies of the diaphragm, abdominal wall or umbilical cord
LB10-LB1ZStructural developmental anomalies of the digestive tract
10 more
LA00Anencephaly or similar anomalies
LA01Cephalocele
LA02Spina bifida
LA03Arnold-Chiari malformation type II
LA04Congenital hydrocephalus
LA05Cerebral structural developmental anomalies
LA06Cerebellar structural developmental anomalies
LA07Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
4B4YOther specified diseases of the immune system
1 more
LA00.0Anencephaly
LA00.1Iniencephaly
LA00.2Acephaly
LA00.3Amyelencephaly
4B4YOther specified diseases of the immune system
4B4ZDiseases of the immune system, unspecified

International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).

Release 2026-01. View this entity in the official WHO ICD-11 browser.

This page reproduces WHO classification content for reference. It is not medical advice and must not be used to diagnose or treat. For coding decisions, consult the official release and your national coding guidelines.

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