Endocardial fibroelastosis

Definition

Endocardial fibroelastosis is the formation of a marked fibro-elastic thickening of the subendocardium in one or both cardiac ventricles. A disorder of fetuses and infants, secondary causes include congenital left-sided obstructive cardiac lesions, metabolic disorders, autoimmune disease (anti-Ro/anti-La antibodies), and transplacental viral infection such as mumps. Primary endocardial fibroelastosis has been linked to recessive and x-linked inheritance, such as with Barth syndrome.

Also indexed as

Nearby in Cardiomyopathy

• BC43.0Dilated cardiomyopathy
• BC43.1Hypertrophic cardiomyopathy
• BC43.2Restrictive cardiomyopathy
• BC43.4Cardiomyopathy due to drugs or other external agents
• BC43.5Stress-induced cardiomyopathy
• BC43.6Arrhythmogenic ventricular cardiomyopathy
• BC43.7Diabetic cardiomyopathy
• 4B4YOther specified diseases of the immune system