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BC44 category

Noncompaction cardiomyopathy

Definition

Noncompaction cardiomyopathy classically involves the left ventricle but can also involve only the right ventricle or both. It can occur as an isolated finding or in association with a dilated, hypertrophic, or mixed cardiomyopathic phenotype. It has been described in association with complex congenital heart disease, coronary artery anomalies and as an isolated finding, with and without musculoskeletal and other system abnormalities.

Also indexed as

Biventricular noncompaction cardiomyopathyFamilial-genetic noncompaction cardiomyopathyLeft ventricular noncompactionLeft ventricular noncompaction cardiomyopathyNoncompaction cardiomyopathyNoncompaction cardiomyopathy associated with congenital heart diseaseNoncompaction cardiomyopathy due to Barth syndromeNoncompaction cardiomyopathy due to Z-line protein/Cypher mutationNoncompaction cardiomyopathy due to Z-line protein/Cypher mutation (Zaspopathy)Noncompaction cardiomyopathy due to laminopathyRight ventricular noncompaction cardiomyopathySarcomeric noncompaction cardiomyopathyX-linked noncompaction cardiomyopathy

Nearby in Diseases of the myocardium or cardiac chambers