ICD·index Chapters ENESDE
8E00 category

Sporadic Creutzfeldt-Jakob Disease

Definition

A disease of the brain, that is associated with a mutation of normal prion protein genes or spontaneous transformation of prion proteins. This disease is characterised by a long incubation period, progressive dementia, neurological deficits, and is fatal. Transmission may be by direct contact with infected nervous tissue or blood. Confirmation is by pathological examination of the brain.

Also indexed as

Classical sporadic Creutzfeldt-Jakob DiseaseCortical sporadic Creutzfeldt-Jakob DiseaseCreutzfeldt-Jakob disease NOSSporadic Creutzfeldt-Jakob DiseaseThalamic sporadic Creutzfeldt-Jakob Diseaseidiopathic Creutzfeldt-Jakob diseasesCJD - [Sporadic Creutzfeldt-Jakob Disease]

Nearby in Human prion diseases