4A01.05
category
Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells
Also indexed as
Activation-induced cytidine deaminase deficiencyHIGM2 - [hyper-IgM syndrome type 2]HIGM5 - [hyper-IgM syndrome type 5]Hyper IgMHyper-IgM syndrome due to AICDA deficiencyHyper-IgM syndrome due to AID deficiencyHyper-IgM syndrome due to UNG - [uracil N glycosylase] deficiencyHyper-IgM syndrome due to uracil N glycosylaseHyper-IgM syndrome type 2Hyper-IgM syndrome type 5Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells
Nearby in Immunodeficiencies with predominantly antibody defects
4A01.00Hereditary agammaglobulinaemia with profoundly reduced or absent B cells4A01.01Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells4A01.02Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells4A01.03Transient hypogammaglobulinaemia of infancy4A01.04Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells4B4YOther specified diseases of the immune system4B4ZDiseases of the immune system, unspecified