4A01.01
category
Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
Definition
This refers to a nonfamilial type of primary immune deficiency disease characterised by a reduction in at least two serum immunoglobulin isotypes. Circulating B cells may be normal or low.
Also indexed as
Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytesHypogammaglobulinaemia NOSImmunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cellsacquired agammaglobulinaemia NOSagammaglobulinaemia NOSagammaglobulinaemia antibody deficiency syndromecommon variable agammaglobulinaemiahypogammaglobulinaemia antibody deficiency syndromeimmunoglobulin-bearing b-lymphocytes agammaglobulinaemianonfamilial agammaglobulinaemianonfamilial hypogammaglobulinaemia
Nearby in Immunodeficiencies with predominantly antibody defects
4A01.00Hereditary agammaglobulinaemia with profoundly reduced or absent B cells4A01.02Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells4A01.03Transient hypogammaglobulinaemia of infancy4A01.04Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells4A01.05Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells4B4YOther specified diseases of the immune system4B4ZDiseases of the immune system, unspecified