Immunodeficiencies with predominantly antibody defects

Definition

A disorder characterised by an inability to mount a normal immune response due to antibody (i.e. immunoglobulin) defects

8 subordinate codes

• 4A01.00Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
• 4A01.01Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
• 4A01.02Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells
• 4A01.03Transient hypogammaglobulinaemia of infancy
• 4A01.04Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells
• 4A01.05Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Primary immunodeficiencies due to disorders of adaptive immunity

• 4A01.1Combined immunodeficiencies
• 4A01.2Diseases of immune dysregulation
• 4A01.3Other well-defined immunodeficiency syndromes due to defects in adaptive immunity
• 4B4ZDiseases of the immune system, unspecified