3A50.02
category
Haemoglobin H disease (– α/– – included)
Definition
Haemoglobin H (HbH) disease is a moderate to severe form of alpha-thalassemia characterised by pronounced microcytic hypochromic haemolytic anaemia.
Also indexed as
Haemoglobin H disease (– α/– – included)HbH - [haemoglobin H] diseasealpha - /- - or mutational forms of alpha-thalassaemiaalpha thalassaemia intermedia
Nearby in Alpha thalassaemia