Langerhans cell sarcoma

Definition

A neoplastic proliferation of Langerhans cells with overtly malignant cytologic features. It can be considered a higher grade variant of Langerhans cell histiocytosis (LCH) and it can present de novo or progress from antecedent LCH.

Also indexed as

Nearby in Histiocytic or dendritic cell neoplasms

• 2B31.0Juvenile xanthogranuloma
• 2B31.1Histiocytic sarcoma
• 2B31.2Langerhans cell histiocytosis
• 2B31.4Interdigitating dendritic cell sarcoma
• 2B31.5Follicular dendritic cell sarcoma
• 2B31.6Indeterminate cell histiocytosis
• 2B31.7Fibroblastic reticular cell tumour
• 4B4YOther specified diseases of the immune system