Ehlers-Danlos syndrome

Definition

Ehlers-Danlos syndrome (EDS) is a heterogeneous group of inherited disorders of connective tissue, principally collagen, that range in severity from mild joint hypermobility to life-threatening fragility of soft tissue and vasculature.

3 subordinate codes

• LD28.10Ehlers-Danlos syndrome, classical type
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Syndromes with connective tissue involvement as a major feature

• LD28.0Marfan syndrome or Marfan-related disorders
• LD28.2Genetically-determined cutis laxa
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified