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Chapters ENES DE

20Developmental anomalies
Multiple developmental anomalies or syndromes
LD28Syndromes with connective tissue involvement as a major feature

LD28.0 category

Marfan syndrome or Marfan-related disorders

4 subordinate codes

LD28.00Congenital contractural arachnodactyly
LD28.01Marfan syndrome
4B4YOther specified diseases of the immune system
4B4ZDiseases of the immune system, unspecified

Nearby in Syndromes with connective tissue involvement as a major feature

LD28.1Ehlers-Danlos syndrome
LD28.2Genetically-determined cutis laxa
4B4YOther specified diseases of the immune system
4B4ZDiseases of the immune system, unspecified

NextLD28.1 — Ehlers-Danlos syndrome

Browse ICD-11

01Certain infectious or parasitic diseases
02Neoplasms
03Diseases of the blood or blood-forming organs
04Diseases of the immune system
05Endocrine, nutritional or metabolic diseases
06Mental, behavioural or neurodevelopmental disorders
07Sleep-wake disorders
08Diseases of the nervous system
09Diseases of the visual system
10Diseases of the ear or mastoid process
11Diseases of the circulatory system
12Diseases of the respiratory system
13Diseases of the digestive system
14Diseases of the skin
15Diseases of the musculoskeletal system or connective tissue
16Diseases of the genitourinary system
17Conditions related to sexual health
18Pregnancy, childbirth or the puerperium
19Certain conditions originating in the perinatal period
20Developmental anomalies
21Symptoms, signs or clinical findings, not elsewhere classified
22Injury, poisoning or certain other consequences of external causes
23External causes of morbidity or mortality
24Factors influencing health status or contact with health services
25Codes for special purposes
26Supplementary Chapter Traditional Medicine Conditions
VSupplementary section for functioning assessment
XExtension Codes
LA00-LD0ZStructural developmental anomalies primarily affecting one body system
LD20-LD2ZMultiple developmental anomalies or syndromes
LD40-LD7ZChromosomal anomalies, excluding gene mutations
LD90Conditions with disorders of intellectual development as a relevant clinical feature
4B4YOther specified diseases of the immune system
4B4ZDiseases of the immune system, unspecified
LD24Syndromes with skeletal anomalies as a major feature
LD25Syndromes with face or limb anomalies as a major feature
LD26Syndromes with limb anomalies as a major feature
LD27Syndromes with skin or mucosal anomalies as a major feature
LD28Syndromes with connective tissue involvement as a major feature
LD29Syndromes with obesity as a major feature
LD2AMalformative disorders of sex development
LD2BSyndromes with premature ageing appearance as a major feature
LD2COvergrowth syndromes
11 more
LD28.0Marfan syndrome or Marfan-related disorders
LD28.1Ehlers-Danlos syndrome
LD28.2Genetically-determined cutis laxa
4B4YOther specified diseases of the immune system
4B4ZDiseases of the immune system, unspecified
LD28.00Congenital contractural arachnodactyly
LD28.01Marfan syndrome
4B4YOther specified diseases of the immune system
4B4ZDiseases of the immune system, unspecified

International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).

Release 2026-01. View this entity in the official WHO ICD-11 browser.

This page reproduces WHO classification content for reference. It is not medical advice and must not be used to diagnose or treat. For coding decisions, consult the official release and your national coding guidelines.

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