20Developmental anomalies
Structural developmental anomalies primarily affecting one body system
Structural developmental anomalies of the circulatory system
LA90Structural developmental anomalies of the peripheral vascular system
LA90.1Lymphatic malformations
LA90.10
category
Macrocystic lymphatic malformation
Definition A condition caused by failure of the lymphatic system to correctly develop during the antenatal period. This condition is characterised by large, soft, smooth clear masses under normal or bluish skin. This condition may be associated with cellulitis, bleeding within the malformation, pain, or leakage of lymphatic fluid internally.
Also indexed as
Cavernous lymphangioma Cavernous lymphatic malformation Circumscribed lymphangioma Circumscribed lymphatic malformation Lymphangiomatous cyst of unspecified site Macrocystic lymphangioma Macrocystic lymphatic malformation
Nearby in Lymphatic malformations
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
About · Data & methodology ·
Privacy · Contact