20Developmental anomalies
Structural developmental anomalies primarily affecting one body system
Structural developmental anomalies of the circulatory system
LA90Structural developmental anomalies of the peripheral vascular system
LA90.5
category
Pulmonary arteriovenous fistula
Definition A congenital cardiovascular malformation in which there is an abnormal, direct connection between a pulmonary artery and pulmonary vein or left atrium without an intervening capillary bed.
Also indexed as
Pulmonary arteriovenous aneurysm Pulmonary arteriovenous fistula Pulmonary arteriovenous malformation
Nearby in Structural developmental anomalies of the peripheral vascular system
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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