ICD·index Chapters ENESDE
LA89.3 category

Hypoplastic left heart syndrome

Definition

A spectrum of congenital cardiovascular malformations with normally aligned great arteries without a common atrioventricular junction, characterised by underdevelopment of the left heart with significant hypoplasia of the left ventricle including atresia, stenosis, or hypoplasia of the aortic or mitral valve, or both valves, and hypoplasia of the ascending aorta and aortic arch.

Also indexed as

HLHS - [hypoplastic left heart syndrome]Hypoplastic left heart syndromeaortic valve atresia, in hypoplastic left heart syndromeascending aorta hypoplasia, in hypoplastic left heart syndromeatresia of mitral valve, in hypoplastic left heart syndromeatresia or marked hypoplasia of aortic orifice or valve, with hypoplasia of ascending aorta and defective development of left ventricleatresia or marked hypoplasia, of aortic orifice or valve, with hypoplasia of ascending aorta and defective development of left ventricle with mitral valve atresiahypoplasia of aortic valve, in hypoplastic left heart syndromehypoplasia of the left heartleft heart hypoplasia syndrome

Nearby in Functionally univentricular heart