ICD·index Chapters ENESDE
FB51.40 category

Primary retroperitoneal fibrosis

Definition

This is the commonest form of retroperitoneal fibrosis. By definition, no associated trigger (e.g. drugs or malignancy) can be determined, although atherosclerosis of the abdominal aorta is often associated. It has been postulated that such atherosclerosis may be of aetiological significance in some cases.

Also indexed as

Chronic periaortitisPrimary retroperitoneal fibrosisidiopathic retroperitoneal fibrosis

Nearby in Retroperitoneal fibrosis