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BC65.5 category

Catecholaminergic polymorphic ventricular tachycardia

Definition

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder of childhood characterised by adrenergically-induced ventricular tachycardia (bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia and atrial fibrillation) manifesting as syncope and sudden death.

Also indexed as

Catecholaminergic polymorphic ventricular tachycardiaCatecholaminergic polymorphic ventricular tachycardia due to Calsequestrin mutationCatecholaminergic polymorphic ventricular tachycardia due to RYR2 mutation

Nearby in Cardiac arrhythmia associated with genetic disorder