BB01.0
category
Pulmonary arterial hypertension
Definition
Pulmonary arterial hypertension is a clinical condition characterised by the presence of pre-capillary pulmonary hypertension in the absence of other causes of pre-capillary pulmonary hypertension, such as due to lung diseases, chronic thromboembolic pulmonary hypertension, or other rare diseases. It includes different forms that share a similar clinical picture and virtually identical pathological changes of the lung microcirculation.
Inclusions
- Idiopathic pulmonary arterial hypertension
- primary pulmonary hypertension
Also indexed as
APAH - [Associated pulmonary arterial hypertension]Arrillaga Ayerza syndromeEisenmenger syndromeFamilial pulmonary arterial hypertensionFamilial pulmonary arterial hypertension due to ALK1 or endoglin mutationsFamilial pulmonary arterial hypertension due to BMPR2 mutationsFamilial pulmonary arterial hypertension of unknown originIdiopathic pulmonary arterial hypertensionPAH - [pulmonary arterial hypertension]Pulmonary arterial hypertensionPulmonary arterial hypertension associated with HIV infectionPulmonary arterial hypertension associated with congenital heart diseasePulmonary arterial hypertension associated with congenital systemic-to-pulmonary shuntPulmonary arterial hypertension associated with connective tissue diseasesPulmonary arterial hypertension associated with other aetiologiesPulmonary arterial hypertension associated with other conditionsPulmonary arterial hypertension associated with portal hypertensionPulmonary arterial hypertension associated with schistosomiasisPulmonary arterial hypertension induced by drugs or toxinsPulmonary capillary haemangiomatosisPulmonary veno-occlusive diseaseheritable pulmonary arterial hypertensionprimary pulmonary hypertension