ICD·index Chapters ENESDE
6D83 category

Frontotemporal dementia

Definition

Frontotemporal dementia (FTD) is a group of primary neurodegenerative disorders primarily affecting the frontal and temporal lobes. Onset is typically insidious with a gradual and worsening course. Several syndromic variants (some with an identified genetic basis or familiality) are described that include presentations with predominantly marked personality and behavioral changes (such as executive dysfunction, apathy, deterioration of social cognition, repetitive behaviours, and dietary changes), predominantly language deficits (that include semantic, agrammatic/nonfluent, and logopenic forms), predominantly movement-related deficits (progressive supranuclear palsy, corticobasal degeneration, multiple systems atrophy, or amyotrophic lateral sclerosis), or a combination of these deficits. Memory function often remains relatively intact, particularly during the early stages of the disorder.

Coding note

This category should never be used in primary tabulation. The codes are provided for use as supplementary or additional codes when it is desired to identify the presence of dementia in diseases classified elsewhere. When dementia is due to multiple aetiologies, code all that apply.

Also indexed as

Dementia in Pick diseaseFTD - [frontotemporal dementia]Frontotemporal dementiaFrontotemporal dementia due to C9orf72 mutationFrontotemporal dementia due to CHMP2B mutationFrontotemporal dementia due to FUS mutationFrontotemporal dementia due to GRN mutationFrontotemporal dementia due to MAPT mutationFrontotemporal dementia due to TARDBP mutationFrontotemporal dementia due to UBS mutationFrontotemporal dementia due to VCP mutationFrontotemporal dementia due to genetic mutationFrontotemporal dementia due to other or new mutationsFrontotemporal dementia with familial inclusion body myopathy with Paget’s disease of boneFrontotemporal dementia with motor neuron diseaseFrontotemporal dementia, behavioural variantFrontotemporal dementia, language variantFrontotemporal dementia, logopenic variantFrontotemporal dementia, non-fluent or agrammatic variantFrontotemporal dementia, semantic variantLogopenic primary progressive aphasiaLogopenic progressive aphasiaPPA - [primary progressive aphasia] agrammaticPPA - [primary progressive aphasia] semanticPick diseasePick disease of brainPrimary progressive aphasiaProgressive aphasiaSemantic dementiadementia in fronto-temporal lobar degenerationfrontal lobe dementiafrontotemporal lobe dementiaprogressive non-fluent aphasiatemple dementia

Nearby in Dementia