05Endocrine, nutritional or metabolic diseases Metabolic disorders Other metabolic disorders 5D00Amyloidosis 5D00.2Hereditary amyloidosis
5D00.21
category
Non-neuropathic heredofamilial amyloidosis
Definition This is an amyloidosis (the formation of insoluble proteins, or amyloids) of inherited origin that does not affect the peripheral nerves. The most common sites of deposits are associated with the kidney and heart.
Also indexed as
Cardiac non-neuropathic heredofamilial amyloidosis Cerebral non-neuropathic heredofamilial amyloidosis angiopathy Non-neuropathic heredofamilial amyloidosis
Nearby in Hereditary amyloidosis
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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