5D00.0
category
AL amyloidosis
Definition
AL (Amyloid Light-Chain) Amyloidosis is due to the deposition of immunoglobulin light chains in glomeruli where they are seen as Congo red binding fibrils and immuno-stain specifically for kappa or lambda light chains. By light microscopy there is amorphous hyaline material in the mesangium and capillary walls. A light chain producing plasma cell or B-cell dysplasia is responsible. Other organs are also involved in this systemic disease.
Also indexed as
AD type amyloidosisAL [Amyloid Light-Chain]AL amyloidosisALECT2 amyloidosisAS transthyretin amyloidosisAmyloid gastrointestinal diseaseAmyloid spinal degenerationAmyloid splenic degenerationAmyloidosis cutis nodularis atrophicansAmyloidosis of liverAmyloidosis of small intestineArthropathy in amyloidosisCardiac organ-limited amyloidosisCholestatic hepatic amyloidosisDanish type amyloidosisDanish type familial amyloid cardiomyopathyDenmark type amyloidosisGlaucoma in amyloidosisGlomerular disorders in organ-limited amyloidosisHepatic amyloidosis with intrahepatic cholestasisImmunoglobulinic amyloidosisInterstitial lung diseases associated with amyloidosisLichen amyloidosisMacular amyloidosisNodular amyloidosisOrgan-limited amyloidosisPapular amyloidosisPrimary amyloidosisPrimary localised cutaneous amyloidosisStiff heart syndromeTumefactive amyloidosisamyloid arthritisamyloid arthropathyamyloid cardiomyopathyamyloid heartamyloid heart degenerationamyloid heart diseaseamyloid heart muscle diseaseamyloid intestinal degenerationamyloid nephritisamyloid splenic diseasearthritis secondary to amyloidosisarticular amyloidcardiac amyloidosisfamilial amyloid cardiomyopathyfamilial amyloid heart diseaseheart amyloidosishepatic amyloidosislocalised amyloid depositlocalised amyloid infiltrationlocalised amyloidosislocalised generalised amyloid infiltrationlocalised generalised amyloidosislocalised primary amyloidosisnephrotic syndrome in amyloidosispulmonary amyloidosissenile cardiac amyloidosis