05Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C53Inborn errors of energy metabolism
5C53.2Disorders of mitochondrial oxidative phosphorylation
5C53.21
category
Multiple mitochondrial DNA deletion syndromes
Definition This is the multiple DNA located in organelles called mitochondria, structures within eukaryotic cells that convert the chemical energy from food into a form that cells can use, adenosine triphosphate (ATP).
Also indexed as
MIRAS - [Mitochondrial recessive ataxic syndrome] Mitochondrial DNA deletion ataxia neuropathy spectrum Mitochondrial recessive ataxic syndrome Multiple mitochondrial DNA deletion syndromes SANDO - [Sensory ataxic neuropathy – dysarthria - ophthalmoparesis] syndrome SCAE - [Spinocerebellar ataxia with epilepsy] Sensory ataxic neuropathy – dysarthria - ophthalmoparesis Spinocerebellar ataxia with epilepsy
Nearby in Disorders of mitochondrial oxidative phosphorylation
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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