Organic aciduria

Definition

An inborn error of metabolism disrupting normal amino acid metabolism, particularly branched-chain amino acids, causing a buildup of acids, which are usually not present

4 subordinate codes

• 5C50.E0Classical organic aciduria
• 5C50.E1Cerebral organic aciduria
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Inborn errors of amino acid or other organic acid metabolism

• 5C50.0Phenylketonuria
• 5C50.1Disorders of tyrosine metabolism
• 5C50.2Disorders of histidine metabolism
• 5C50.3Disorders of tryptophan metabolism
• 5C50.4Disorders of lysine or hydroxylysine metabolism
• 5C50.5Disorders of the gamma-glutamyl cycle
• 5C50.6Disorders of serine metabolism
• 5C50.7Disorders of glycine metabolism