5C50.A
category
Disorders of urea cycle metabolism
Exclusions
- Disorders of ornithine metabolism
(5C50.9) - Lysinuric protein intolerance
(4B4Y)
6 subordinate codes
Nearby in Inborn errors of amino acid or other organic acid metabolism
5C50.0Phenylketonuria5C50.1Disorders of tyrosine metabolism5C50.2Disorders of histidine metabolism5C50.3Disorders of tryptophan metabolism5C50.4Disorders of lysine or hydroxylysine metabolism5C50.5Disorders of the gamma-glutamyl cycle5C50.6Disorders of serine metabolism5C50.7Disorders of glycine metabolism