ICD·index Chapters ENESDE
4A44.A1 category

Granulomatosis with polyangiitis

Definition

Necrotizing granulomatous inflammation usually involving the upper and lower respiratory tract, and necrotizing vasculitis affecting predominantly small to medium-sized vessels (e.g., capillaries, venules, arterioles, arteries and veins). Necrotizing glomerulonephritis is common.

Inclusions

  • Wegener granulomatosis

Also indexed as

Granulomatosis with polyangiitisNecrotising respiratory granulomatosisWegener granulomatosis

Nearby in Antineutrophil cytoplasmic antibody-associated vasculitis