Vasculitis

Definition

Vasculitides represent a heterogenous group of diseases of multifactorial aetiology characterised by inflammatory lesions of vessels. These lesions consist of fibrinoid necrosis (necrotizing arteritis), giant cell infiltration without necrosis, immunoglobulins deposit or leukocytoclastic infiltration. The spectrum and severity of the systemic vaculitides is broad, from life or sight threatening fulminant disease to relatively minor skin disease.

14 subordinate codes

• 4A44.0Rhizomelic pseudopolyarthritis
• 4A44.1Aortic arch syndrome
• 4A44.2Giant cell arteritis
• 4A44.3Single organ vasculitis
• 4A44.4Polyarteritis nodosa
• 4A44.5Mucocutaneous lymph node syndrome
• 4A44.6Sneddon syndrome
• 4A44.7Primary angiitis of the central nervous system
• 4A44.8Thromboangiitis obliterans
• 4A44.9Immune complex small vessel vasculitis
• 4A44.AAntineutrophil cytoplasmic antibody-associated vasculitis
• 4A44.BLeukocytoclastic vasculitis
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Nonorgan specific systemic autoimmune disorders

• 4A40Lupus erythematosus
• 4A41Idiopathic inflammatory myopathy
• 4A42Systemic sclerosis
• 4A43Overlap or undifferentiated nonorgan specific systemic autoimmune disease
• 4A45Antiphospholipid syndrome
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified