4A43.0
category
IgG4 related disease
Definition
IgG4 related syndrome (IgG4-related disease: IgG4-RD) is a clinical disease characterised by elevated serum IgG4 concentration and tumefaction or tissue infiltration by IgG4-positive plasma cells. The diagnostic criteria for IgG4 related syndrome have been proposed, and it may be present in a certain population of patients with a wide variety of diseases, including Mikulicz disease, autoimmune pancreatitis, hypophysitis, Riedel thyroiditis, interstitial pneumonitis, interstitial nephritis, prostatitis, lymphadenopathy, retroperitoneal fibrosis, inflammatory aortic aneurysm, and inflammatory pseudo tumour.
Also indexed as
Cholangitis of IgG4-related sclerosing diseaseCutaneous pseudolymphomaEosinophilic angiocentric fibrosisIgG4 related diseaseIgG4-related aortitisIgG4-related dacryoadenitis and sialadenitisIgG4-related hepatopathyIgG4-related kidney diseaseIgG4-related mediastinitisIgG4-related mesenteritisIgG4-related ophthalmic diseaseIgG4-related pachymeningitisIgG4-related retroperitoneal fibrosisIgG4-related sclerosing cholangitisIgG4-related submandibular gland diseaseIgG4-related thyroid disease