04Diseases of the immune system
Nonorgan specific systemic autoimmune disorders
4A42Systemic sclerosis
4A42.0
category
Paediatric onset systemic sclerosis
Definition Systemic sclerosis arising before the age of 16. Involvement of internal organs is less common but arthritis and myositis are more common than in adults.
Also indexed as
Diffuse paediatric systemic sclerosis Limited paediatric systemic sclerosis Paediatric onset systemic sclerosis
Nearby in Systemic sclerosis
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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