4A41.21
category
Noninflammatory inclusion body myopathy
Definition
Noninflammatory inclusion body myopathy (IBM) is an idiopathic muscle disorder without inflammatory exudates and expression of class I major histocompatibility complex. Rimmed vacuoles and “IBM-like” filaments without inflammatory cells are described in muscle biopsy.
Exclusions
Also indexed as
Desmin-related myopathy with Mallory body-like inclusionsHIBM - [hereditary inclusion body myositis]Hereditary inclusion body myopathyHereditary inclusion body myopathy - joint contractures - ophthalmoplegiaIBMPFD - [inclusion body myopathy with Paget disease of bone and frontotemporal dementia]Inclusion body myopathy with Paget disease of bone and frontotemporal dementiaNoninflammatory inclusion body myopathySporadic inclusion body myopathyX-linked myopathy with excess autophagyXMEA - [x-linked myopathy with excess autophagy]