04Diseases of the immune system Nonorgan specific systemic autoimmune disorders 4A40Lupus erythematosus 4A40.0Systemic lupus erythematosus
4A40.00
category
Systemic lupus erythematosus with skin involvement
Definition Systemic lupus erythematosus (SLE) involving the skin. This may present with a malar "butterfly" erythema or with extensive necrolysis of sun-exposed skin, particularly on the head, neck and upper torso.
Also indexed as
Acute cutaneous lupus erythematosus Systemic lupus erythematosus skin rash Systemic lupus erythematosus with skin involvement
Nearby in Systemic lupus erythematosus
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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