04Diseases of the immune system
Primary immunodeficiencies
4A01Primary immunodeficiencies due to disorders of adaptive immunity
4A01.3Other well-defined immunodeficiency syndromes due to defects in adaptive immunity
4A01.30
category
Immunodeficiency due to defects of the thymus
Also indexed as
Congenital thymic dysplasia syndrome Immunodeficiency due to absence of thymus Immunodeficiency due to defects of the thymus Nezelof syndrome Thymic aplasia
Nearby in Other well-defined immunodeficiency syndromes due to defects in adaptive immunity
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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