ICD·index Chapters ENESDE
3B62.4 category

Alpha-delta dense granule deficiency

Definition

A condition caused by determinants arising after birth, in the antenatal period. This condition is characterised by defects in the alpha delta dense granules in platelets, leading to abnormalities in coagulation mechanisms. This condition may present with prolonged bleeding, epistaxis, menorrhagia, easy bruising, anaemia, fatigue or shortness of breath. Confirmation is by identification of low levels of alpha delta dense granules in a blood sample.

Also indexed as

Alpha-delta dense granule deficiencydeficient alpha granule syndromeplatelet alpha granule deficiency

Nearby in Qualitative platelet defects