ICD·index Chapters ENESDE
3B15 category

Inherited coagulation factor deficiency without bleeding tendency

Definition

A disease caused by a genetically inherited mutation leading to decreased levels of coagulation factor. This disease is characterised by decreased levels of coagulation factor without leading to increased haemorrhaging. Confirmation is by identification of decreased levels of coagulation factor in a blood sample.

Also indexed as

Congenital Hageman factor deficiencyCongenital high-molecular-weight kininogen deficiencyCongenital prekallikrein deficiencyDeficiency of factor XIIHageman defectHageman deficiencyHageman factor defectHageman factor deficiencyHereditary factor XII deficiencyInherited coagulation factor deficiency without bleeding tendencycongenital factor XII deficiencyfactor XII deficiency disease

Nearby in Congenital or constitutional haemorrhagic condition