ICD·index Chapters ENESDE
3A10.2 category

Hereditary elliptocytosis

Definition

Hereditary elliptocytosis is a group of rare conditions caused by abnormalities in the red cell cytoskeleton and marked by the presence on blood smears of numerous elliptical red blood cells, called elliptocytes. Clinical presentations are highly heterogeneous ranging from asymptomatic forms to more severe forms associated with variable anaemia, from moderate to severe and with pyropoikilocytosis including fragmented red cells, microelliptocytes and microspherocytes.

Inclusions

  • Common hereditary elliptocytosis
  • Hereditary pyropoikilocytosis
  • Homozygous hereditary elliptocytosis
  • Spherocytic elliptocytosis

Also indexed as

Common hereditary elliptocytosisCommon heterozygous hereditary elliptocytosisHE - [hereditary elliptocytosis]Hereditary elliptocytosisHereditary elliptocytosis with infantile poikilocytosisHereditary pyropoikilocytosisHomozygous hereditary elliptocytosisSpherocytic elliptocytosiscongenital elliptocytosiscongenital ovalocytosiselliptocytosiselliptocytosis anaemiahereditary ovalocytosisoval erythrocytosisovalocytosis

Nearby in Hereditary haemolytic anaemia