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Chapters ENES DE

XExtension Codes
Substances
XM6S30Medicaments
XM4TG8Agents primarily affecting water and nutrition-balance or metabolism
Enzymes and digestants

XM8F43 category

Pegvaliase

Also indexed as

Pegvaliase

Nearby in Enzymes and digestants

XM7KX6Chenodeoxycholic acid
XM8MG9Ursodeoxycholic acid
XM37T5Cholic acid
XM1F53Diastase
XM5888Multienzymes
XM3UE5Pepsin
XM6F61Hydrochloric acid
XM3RH9Citric acid

PreviousXM3FP4 — Vestronidase alfa NextXM30U5 — Pegunigalsidase alfa

Browse ICD-11

01Certain infectious or parasitic diseases
02Neoplasms
03Diseases of the blood or blood-forming organs
04Diseases of the immune system
05Endocrine, nutritional or metabolic diseases
06Mental, behavioural or neurodevelopmental disorders
07Sleep-wake disorders
08Diseases of the nervous system
09Diseases of the visual system
10Diseases of the ear or mastoid process
11Diseases of the circulatory system
12Diseases of the respiratory system
13Diseases of the digestive system
14Diseases of the skin
15Diseases of the musculoskeletal system or connective tissue
16Diseases of the genitourinary system
17Conditions related to sexual health
18Pregnancy, childbirth or the puerperium
19Certain conditions originating in the perinatal period
20Developmental anomalies
21Symptoms, signs or clinical findings, not elsewhere classified
22Injury, poisoning or certain other consequences of external causes
23External causes of morbidity or mortality
24Factors influencing health status or contact with health services
25Codes for special purposes
26Supplementary Chapter Traditional Medicine Conditions
VSupplementary section for functioning assessment
XExtension Codes
Histopathology
Dimensions of injury
Dimensions of external causes
Consciousness
Substances
Diagnosis code descriptors
Capacity or context
Health Devices, Equipment and Supplies
Extension codes of particular relevance to skin diseases
5 more
XM6S30Medicaments
XM9N55Substances, chiefly nonmedicinal
Allergens
XM6WT8Agents primarily affecting blood constituents or immune system
XM3KY1Agents affecting genitourinary system, sex or anabolic hormones
XM26S4Hormones and their synthetic substitutes or antagonists, not elsewhere classified
XM9W63Agents affecting bones, joints or other connective tissue, not elsewhere classified
XM4TG8Agents primarily affecting water and nutrition-balance or metabolism
XM3973Agents primarily affecting the cardiovascular system
XM6CH2Drugs primarily affecting the autonomic nervous system
XM7YD4Drugs used in addictive disorders
XM8014Antivertigo and motion sickness preparations
14 more
Mineral salts and supplements, not elsewhere classified
Electrolytic, caloric and water-balance agents
Diuretics
Mineralocorticoids
Vitamins and antioxidants
Enzymes and digestants
Agents in bile and liver therapy
Antiobesity preparations
Drugs used to treat enzyme deficiencies and disorders of aminoacid, glycolipid and glycoprotein metabolism
1 more
XM11U1Galsulfase
XM3Z98Idursulfase
XM8J61Velaglucerase alfa
XM8HN5Taliglucerase alfa
XM7QH6Elosulfase alfa
XM5U98Asfotase alfa
XM6UN5Sebelipase alfa
XM5U91Velmanase alfa
XM98F5Idursulfase beta
XM9L40Cerliponase alfa
XM3FP4Vestronidase alfa
XM8F43Pegvaliase
XM30U5Pegunigalsidase alfa
XM56M4Atidarsagene autotemcel
XM9F01Avalglucosidase alfa
18 more

International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).

Release 2026-01. View this entity in the official WHO ICD-11 browser.

This page reproduces WHO classification content for reference. It is not medical advice and must not be used to diagnose or treat. For coding decisions, consult the official release and your national coding guidelines.

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